Budd-Chiari syndrome is a rare disorder characterized by hepaticoutflow occlusion and caused by various conditions including congenital or idio-pathic obstruction, hepatic vein thrombosisdue to hypercoagulative state, hepatic veno-occlusive disease after liver transplantation, and hepatic tumors . The major symptoms include ascites, hepatomegaly, and abdominal pain. It has been classified into three types according to the location of the occlusion [25, 26]. Type 1 is defined as occlusion of the inferior vena cava with or without hepatic vein occlusion;type 2,occlusion of major hepatic veins; and type 3, obstruction of the small centrilobular venules (hepatic veno-occlusive dis-ease).From the clinical point of view, Budd-Chiari syndrome should be classified according to whether it can be treated with anticoagulants, surgery, or interventional procedures. In planning treatment, it is important to determine the location and length of hepatic outflow obstruction , and contrast-enhanced 3D MR portographyis an accurate means of doing this. No hepatic veins can be visualized in hepatic veno-occlusive disease, whereas narrowing of the intrahepatic portal vein may be seen with a delayed circulationtime.
Was this article helpful?